Saturday, April 25, 2015

ץ? Ǿ ɤ Ф Ū Ǿ ݸ Ѥ 3 ݸ ˡ Ϥ 뤫 40 Ǿ ز 4 ɤ ƽդˤʤ ʤ Ρ 2 ɤ Ū ز ŷƲ ء 2 Ǿ ز 2015 ʥ ӥ 2 ڶ ľ ȥ ե


Ƨ ư ϡ ǧ ε ǽ 㳲 ɾ ȤȤ ϥ ȥ HD ˤν פ ħ Ǥ 롥 ȯ и ADL 㳲 ž ݤδ? ᡤ νŸ 餹 HD Ǥ Ƨ ư μ ŤϤȤƤ ڤǤ 롥 Ƨ ư ο в Ū طʤ ʣ ǡ ʬ Ƥ ʤ Ū ˤϥɥѥߥ 䥰 륿 ߥ ã ΰ ˤ ꡤ Τ Ǿ 㳲 Ƨ ư ȹ Ƥ 롥 ޤǾ嵭 ؤ ãʪ Τ Ƥ 졤 Ū ȥ쥹 䥰 륿 ߥ ˤ 붽ʳ к ɸŪ Ȥ ݸ Ƥ Ƥ Ū ŤϤʤ ơ ƹ гز ˤ HD Ƨ ư Ф ʪ ˡ Υ ɥ饤 ޤȤ HD Ԥˤߤ Ƨ ư μ ŤȤ ơ Ω 줿ɾ ˤ ä ǧ Ƥ ޤϲ פ Ƥ Ƥ 롥systematic review ϡ 2011ǯ2 ޤǤ ȯɽ 졤 ʤ Ȥ 20 Ͱʾ оݤȤ ʸ Ф ƹԤʤ 줿 ɾ Ȥ Ƥ Unified Huntington's Disease Rating Scale UHDRS ˤ Ѥ 줿 106 28 Ƨ ư Ф Τǡ 塤 δ ͻ Ƨ ư ɾ 롥 礭 ɽžɡ θ Ǽ Ÿ 礭 Ƥ ˡ Ĺ Ū ѡ 12 Ķ ˤ û Ū ѡ 12 ʲ ˤ ʬ ơ ޤ ѤˤĤ Ƹ Ƥ Ƥ 롥 ɾ оݤȤʤä ޤϰʲ ΤȤ Ǥ 롥 A. ɥѥߥ Ĵ ƥȥ ʥ ʾ Υ ߥ ȥ ݡ ޤǡ ɥѥߥ Ѥ ġˡ ? ԥ 귿 B. 륿 ߥ Ĵ ޥ ʹ Τ Υɥѥߥ ʡˡ 륾 ʥ 륿 ߥ γ ѡ C. 륮 ʪ ڥ 롤 쥢 D. ɥ ڥ 롤 Q10 ߥΥ ʥӥ ʹ ʥӥΥ ɡ 侩 ϰʲ 6 ܤǤ 롥 1. ƥȥ ʥ 100 mg/day , ޥ 300–400 mg/day , 륾 200 mg/day ˤ Level B . Ȥ ƥȥ ʥ 륾 Ϥ ˤĤ . ޥ θ ѤΥ å פǡ ƥȥ ʥ ǤϤ ġ ѡ 륾 Ǥϴι Ǿ徺 դ . 2. ʥӥ Ƨ ư 뤬 Level C ˡ Ȥ Ѥζ 줬 ˤ Ĺ Ѥϴ ʤ Level U . 3. 륾 200 mg/day Ƨ ư 뷹 뤬 100mg Ǥ ʾ θ Ĺ Ū ʤ Level B ˡ 4. ڥ Level B ˡ ߥΥ Level B ˡ 쥢 Level C ˤ Ϥʤ 5. Q10 ʾ Ϥʤ Level B ˡ 6. ? ԥ , ο м ɥ ڥ θ Ǥ Level U ˡ ʤߤ ƥȥ ʥ FDA HD Ф ǧ Ĥ ޤǤ ꡤ Ŭ ѤȤ Ȥˤʤ롥 ޤ ܥ ɥ饤 Ȥ Ƥϡ оݤ Բ ǽ ADL ݤ Ƥ 䡤 Τ ġ ǧ ξɤ ǧ ʤ оݤȤ Ƥ 뤿 ᡤ ʹԴ ޤ Τ ƤϤ ʤ ȡ Ū յ Τ UHDRS κǾ ʬ äƤ ʤ ȡ Ť Ф 뼫 ʷ 䡤 и ʥƥȥ ʥ , 륾 롤 ʥӥ Ϲ ˤˤĤ Ƥ Ǥ 뤳 Ȥ 롥 Υ ɥ饤 ɤ ǡ ܤȤϤ ޤ 㤦 פȻפä ΤǤϤʤ ? ͳ Ȥ 2 ĤΤ Ȥ פ Ĥ ҤȤĤϡ ܤ Ū Ѥ Ƥ м ? ԥ ȸ ʤ Ǥ 롥 ? ԥ Τ ˡ ץ ɡʥ ޥ ˤ Ф 2 Ĥλ 褦 Ω 줿ɾ 뤬 Ѥ Ƥ ʤ ä Ĥޤ ܤǻ Ѥ Ƥ м ϡ ӥǥ ϳ Ω Ƥ 餺 ѤȤ Τ ѡ ब ɤΤ褦 ʱƶ Ƥ Τ ʤޤ Ĺ Ѥ Ƥ Ȥ Ȥ Ĥ ͳ ϡ Ǥϡ ݸ Ǥʤ о ˡ ˤĤ Ƥμ Ÿ 椬 Ԥ ƹԤ Ƥ 뤿 Ǥ 롥 ܤǤϿ ޤβ 漫 Τ ʤ Ԥ 줿 Ȥ Ƥ Ť ο ݸ ȯ Τǡ ޤ ɾ Ǻ äƤ פ о ˡ θ 椬 ʬ ǤϤʤ ǽ 롥 Τ褦 ʸ ο ʤȥ ݡ Ȥ ɬ פ Ȼפ ʤߤ ƥȥ ʥ Xenazine Nitoman ξ Dz ꥫ ʤɤ 䤵 Ƥ 뤬 ܤǤ ǯ 侵ǧ ϫ ʤ Ф Ƥ 롥 Pharmacologic Treatment of Chorea in Huntington Disease Evidence-based guidline: Pharmacologic treatment of chorea in Huntington disease Neurology 79; 597-603, 2012
Ǿ ɤ ͽ ͽ ץ? Ǿ ɤ Ф Ū Ǿ ݸ ... ǯ ڰ ɡ ʿ ˤΰ Ū װ ƥ? ɥߥ ѥ ϸ ǤǤ 뤫 ɤ ƽդˤʤ ʤ Ρ Pull test ʤɤ äƻ ȿ 㳲 Ф褤 Τ ͼ ɸ ؤ н ˡ ȿ ȥϥ ޡ Ǿ ɼ Ť Ǥ Ԥˤ ȯ μ š Ǿ ...
ץ? Ǿ ɤ Ф Ū Ǿ ݸ Ѥ 3 ݸ ˡ Ϥ 뤫 40 Ǿ ز 4 ɤ ƽդˤʤ ʤ Ρ 2 ɤ Ū ز ŷƲ ء 2 Ǿ ز 2015 ʥ ӥ 2 ڶ ľ ȥ ե ȵ Կ ڰ ɤ Brugada ɸ ˤ 褷 3 Ǿ ɼ Ťο ȯ 1 η ϲ ˡ ǽ ˤ CT ܥ ѡ ߵ 3 ALS ȴ Ǿɡ Ǿɤϼ Ѥ ƤϤ ʤ 4 ˤ Ƭ ˡ Ǿ Ȥ к 4 ǧ ξɤ Ǿ Ѥ ǧ ξɳز ؽѽ 5
Recent Entries | Ƨ ˤ 뼫 ȱ Ƨ Ƨ 2 BHC2 ˤϥ ѥ TDP43 Ѱ ϥϥ ȥ ɽ 褷 롩 Ƨ ܤ 줿 ꥪ Ρ ϥϥ ȥ ǥ ޥ ... Ƨ L-DOPA ϥ ȥ ΰ Ǥ ȯ ǯ Ʊ ˤ ... ϥ ȥ Ф 쥢 Ťη ϥ ȥ ǥ ޥ ˤ Ǣ ȯ ɵ Ⱦ Ƨ FDG-PET study
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ץ? Ǿ ɤ Ф Ū Ǿ ݸ Ѥ ݸ ˡ Ϥ 뤫 40 Ǿ ز ɤ ƽդˤʤ ʤ Ρ ɤ Ū ز ŷƲ ء ɡ MSA ˤ Ф 饵 Ԥ 줿 Ρ Ǿ ز 2015 ʥ ӥ ڶ ľ ȥ ե ȵ Կ ڰ ɤ Brugada ɸ ˤ 褷 Ǿ ɼ Ťο ȯ 1 η ϲ ˡ ǽ ˤ CT ܥ ѡ ߵ ALS ȴ Ǿɡ Ǿɤϼ Ѥ ƤϤ ʤ ˤ Ƭ ˡ Ǿ Ȥ к
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